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DeCS
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Descriptor English:
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Cerebroside-Sulfatase
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Descriptor Spanish:
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Cerebrósido Sulfatasa
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Descriptor Portuguese:
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Cerebrosídeo Sulfatase
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Synonyms English:
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Arylsulfatase A
Sulfatidate Sulfatase
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Tree Number:
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D08.811.277.352.827.070.250
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Definition English:
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An enzyme that catalyzes the hydrolysis of cerebroside 3-sulfate (sulfatide) to yield a cerebroside and inorganic sulfate. A marked deficiency of arylsulfatase A, which is considered the heat-labile component of cerebroside sulfatase, has been demonstrated in all forms of metachromatic leukodystrophy (LEUKODYSTROPHY, METACHROMATIC). EC 3.1.6.8. |
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Indexing Annotation English:
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/defic: consider also LEUKODYSTROPHY, METACHROMATIC
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See Related English:
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Leukodystrophy, Metachromatic
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History Note English:
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87(76); was see under SULFATASES 1976-86
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Allowable Qualifiers English:
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Record Number:
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2592
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Unique Identifier:
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D002553
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Occurrence in VHL:
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Similar:
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DeCS CID-10 SciELO LILACS LIS
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