Search on: GALACTOSYLCERAMIDES 
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Descriptor English:   Galactosylceramides 
Descriptor Spanish:   Galactosilceramidas 
Descriptor Portuguese:   Galactosilceramidas 
Synonyms English:   Galactocerebrosides
Galactosyl Ceramides  
Tree Number:   D02.065.313.250.450
D09.400.410.420.525.200.250.450
D10.390.470.675.200.250.450
D10.570.877.360.612.200.250.450
Definition English:   Cerebrosides which contain as their polar head group a galactose moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue, due to a defect in beta-galactosidase, is the cause of galactosylceramide lipidosis or globoid cell leukodystrophy. 
History Note English:   91(79); was see under CEREBROSIDES 1979-90 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AG agonists AN analysis
AI antagonists & inhibitors BI biosynthesis
BL blood CF cerebrospinal fluid
CS chemical synthesis CH chemistry
CL classification CT contraindications
DF deficiency DU diagnostic use
EC economics GE genetics
HI history IM immunology
IP isolation & purification ME metabolism
PK pharmacokinetics PD pharmacology
PH physiology PO poisoning
RE radiation effects SE secretion
ST standards SD supply & distribution
TU therapeutic use TO toxicity
UR urine  
Record Number:   5837 
Unique Identifier:   D005699 

Occurrence in VHL:
 

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