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MOSCHKOWITZ DISEASE
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DeCS
Descriptor
English
:
Purpura, Thrombotic Thrombocytopenic
Descriptor
Spanish
:
Púrpura Trombocitopénica Trombótica
Descriptor
Portuguese
:
Púrpura Trombocitopênica Trombótica
Synonyms
English
:
Purpura, Thrombotic Thrombopenic
Moschkowitz Disease
Thrombotic Thrombocytopenic Purpura, Congenital
Thrombotic Thrombocytopenic Purpura, Familial
Tree Number:
C15.378.100.802.687.680
C15.378.140.855.925.750.680
C15.378.925.850
C23.550.414.950.687.680
C23.888.885.687.687.680
Definition
English
:
An acquired, congenital, or familial disorder caused by
PLATELET AGGREGATION
with
THROMBOSIS
in terminal
arterioles
and
capillaries
. Clinical features include
THROMBOCYTOPENIA
; HEMOLYTIC
ANEMIA
;
AZOTEMIA
;
FEVER
; and thrombotic microangiopathy. The classical form also includes neurological
symptoms
and end-organ damage, such as RENAL FAILURE.
History Note
English
:
1986; use PURPURA, THROMBOTIC THROMBOPENIC 1965-1985
Allowable Qualifiers
English
:
BL
blood
CF
cerebrospinal fluid
CI
chemically induced
CL
classification
CO
complications
CN
congenital
DI
diagnosis
DH
diet therapy
DT
drug therapy
EC
economics
EM
embryology
EN
enzymology
EP
epidemiology
EH
ethnology
ET
etiology
GE
genetics
HI
history
IM
immunology
ME
metabolism
MI
microbiology
MO
mortality
NU
nursing
PS
parasitology
PA
pathology
PP
physiopathology
PC
prevention & control
PX
psychology
RA
radiography
RI
radionuclide imaging
RT
radiotherapy
RH
rehabilitation
SU
surgery
TH
therapy
US
ultrasonography
UR
urine
VE
veterinary
VI
virology
Record Number:
12133
Unique Identifier:
D011697
Occurrence in VHL
:
Similar:
DeCS
CID-10
SciELO
LILACS
LIS